Case report on Management and Complication of Peutz Jegher Syndrome

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چکیده

Introduction: Infrequent and characterized by mucocutaneous pigmentations, gastrointestinal polyposis, an increased risk of malignancy, Peutz-Jeghers syndrome is autosomal dominant genetic condition. The usual perioral macules patches that are colored in the buccal mucosa present 90% patients, numerous but not continuously contiguous lesions, primarily (G.I.) tract, with rarely more than 20 hamartomata's polyps, characteristics (P.J.S.). Present complaints Investigation:-Suddenly felt sick to my stomach started puke. Abdominal pain, Black stools, repeated vomiting, weight loss 5 kg 15 days, appetite, Intussusception were discovered during examinations upper small bowel. A thorough study tract was conducted. Endoscopically, enormous polyps duodenum biopsied. Resulting bleeding due G.I. she became anemic. There polyps. Later removed endoscopically while being sedated, C.T.'s Abdomen pelvis found multiple mildly enhanced polypoidal lesions notes attached pyloric part proximal jejunal loops, similar Ascending colon, transverse advice colonoscopy. History: patient admitted 2015 And Operated on 26/12/2015, year Jejunoileal intussusception. primary diagnosis, therapeutic intervention, outcomes: After physical examination investigation, Hamartomatous polyp (P-J Secondary Intussuseception ) Conclusions: following reason for patient's hospital admission. Upon entry hospital, main complaint Peutz Jegher Syndrome identified as condition once all investigations complete. now needs appropriate medical attention quality nursing care.

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ژورنال

عنوان ژورنال: Journal of Pharmaceutical Negative Results

سال: 2022

ISSN: ['0976-9234', '2229-7723']

DOI: https://doi.org/10.47750/pnr.2022.13.s07.166