Case report on Management and Complication of Peutz Jegher Syndrome
نویسندگان
چکیده
Introduction: Infrequent and characterized by mucocutaneous pigmentations, gastrointestinal polyposis, an increased risk of malignancy, Peutz-Jeghers syndrome is autosomal dominant genetic condition. The usual perioral macules patches that are colored in the buccal mucosa present 90% patients, numerous but not continuously contiguous lesions, primarily (G.I.) tract, with rarely more than 20 hamartomata's polyps, characteristics (P.J.S.). Present complaints Investigation:-Suddenly felt sick to my stomach started puke. Abdominal pain, Black stools, repeated vomiting, weight loss 5 kg 15 days, appetite, Intussusception were discovered during examinations upper small bowel. A thorough study tract was conducted. Endoscopically, enormous polyps duodenum biopsied. Resulting bleeding due G.I. she became anemic. There polyps. Later removed endoscopically while being sedated, C.T.'s Abdomen pelvis found multiple mildly enhanced polypoidal lesions notes attached pyloric part proximal jejunal loops, similar Ascending colon, transverse advice colonoscopy. History: patient admitted 2015 And Operated on 26/12/2015, year Jejunoileal intussusception. primary diagnosis, therapeutic intervention, outcomes: After physical examination investigation, Hamartomatous polyp (P-J Secondary Intussuseception ) Conclusions: following reason for patient's hospital admission. Upon entry hospital, main complaint Peutz Jegher Syndrome identified as condition once all investigations complete. now needs appropriate medical attention quality nursing care.
منابع مشابه
Peroperative enteroscopy and polypectomy in Peutz-Jegher syndrome.
We report a 32-year-old who lady when presented with anemia and was detected to have Peutz-Jegher syndrome. She had malignancies of the colon and ovary over a 2-year follow up and was successfully managed. On screening the family two more members were confirmed to have Peutz-Jeghers syndrome and have been put on surveillance.
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Peutz-Jeghers syndrome (PJS) is an unusual hamartomatous polyposis of the gastro intestinal (GI) tract, with pigmentation around lips and macules on the buccal mucosa. The case of a 10-year-old girl who presented with intussusception is reported. A polyp was found to be the cause of an invagination. Histologically it was a hamartoma. PJS is a rare syndrome inherited in an autosomal dominant pat...
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ژورنال
عنوان ژورنال: Journal of Pharmaceutical Negative Results
سال: 2022
ISSN: ['0976-9234', '2229-7723']
DOI: https://doi.org/10.47750/pnr.2022.13.s07.166